Sindrom Von Hippel–Lindau
https://doi.org/10.14341/2071-8713-4955
Abstract
Von Hippel-Lindau syndrome - a systemic disease manifesting with multiple tumor growth, inherited by autosomal-dominant type with high penetrance. Understanding the pathogenesis of the disease is important for determining the start time of screening for the presence of the tumors and adequate treatment, including metabolic disorders.
About the Authors
E Ershova
Endocrinology Research Centre, Moscow
Russian Federation
Russian Federation
M Yukina
Endocrinology Research Centre, Moscow
Russian Federation
Russian Federation
Ekaterina Troshina
Endocrinology Research Centre, Moscow
Russian Federation
Russian Federation
Dmitriy Bel'tsevich
ФГУ "Эндокринологический научный центр" Минздравсоцразвития России, Москва
Russian Federation
Russian Federation
E Mustafaeva
Endocrinology Research Centre, Moscow
Russian Federation
Russian Federation
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